Cryosurgery technique Tissue destruction by local application of a refrigerant offers clear advantages over other invasive methods. Its inherent anesthetic and haemostatic properties make it suitable for outpatient use. The tissue destruction is essentially well circumscribed, leaving a cryolesion characterized by healing without scarring and complications.
Distinct benefits to patients
- Cryo applications under local anesthesia.
- No scarring.
- No bleeding during and after the procedures.
- Palliation of painful neoplasms.
- Minimum pain controlled with non–narcotic analgesics.
- Well accepted by elderly and debilitated patients.
- No unpleasant odor of burning tissue.
- Excellent response, low costs, and minimum hospitalization requirements make cryotherapy a popular modality in ENT surgery.
- Crysurgery in Otorhinolaryngology.
Nasopharyngeal Rhabdomyosarcoma, a common soft tissue sarcoma in children, is a rare identity, so far only four–cases have been reported as per the review of literature. Ours is the fifth case presented exclusively in the nasopharnx, which is, hereby reported. The prognosis of this clinical entity is always gloomy and the modality of the treatment is always surgery, chemotherapy and radiotherapy.
A 5 year old boy was referred to ENT department of K.E.M. hospital with the complaints of nasal obstruction, noisy breathing and mouth breathing for over four months. There was no history of bleeding from the nose or any other significant ENT problems. Clinical examination revealed both nostrils clear with no evidence of any nasal mass occluding the nasal passage. Airways were blocked. Posterior rhinoscopy revealed huge polypoidal and grape like mass arising from the nasopharynx and hanging in the oropharynx pushing the soft palate downward and forward. Palatal movements were normal and there was no neurological involvement. Rest of the ENT examination was insignificant. Rest of the ENT examination was insignificant. Routine hematological tests and urine exam was normal. X–ray nasopharynx and compromising the nasal airway. Provisional diagnosis of nasopharyngeal malignancy was made. CT scan could not be done because of poor economical status of the patient. He was advised surgery and was subjected to excision under G. A. with routine tonsillectomy position. With Boyle–Davis gag, mouth was opened and with adenoid curette the whole mass was curetted. Bleeding was not alarming and controlled with post nasal packing. Postoperative recovery was uneventful. The mass sent for histopathology revealed rhabdomyosarcoma. Patient was advised post–op radiation and chemotherapy. Post operative recovery was uneventful and his symptoms of mouth breathing noisy breathing and nasal obstruction was cleared.
Rhabdomyosarcoma is a highly malignant tumor of childhood arising from the rhabdomyosarcoma of mesenchymal connective tissue. It frequently involves the head and neck region as orbit, nasopharynx, cheek, external ear, maxilla, tonsillar area and soft palate.
The presentation in the nasopharynx is very rare. Only four cases so far have been reported in the literature. Ours is another rare case which exclusively presented in the nasopharynx.
The first mention of this pathological entity was made by Weber (1855), Mason and Soule (1956). The histological classification was made by Wills R. A. (1967). Histologically, the tumor is characterized by round or spindle cells with distinct granular vacuolated cyto plasm.
The Rhabdomyosarcomas can be divided into four subtypes
- Embryonal and embroyonal botryoid.
The prognosis of rhabdomyosarcoma is very gloomy with less than 10% long time survival. The treatment modality adopted is a nutimodality therapy. This entails surgery, chemotherapy and radiotherapy.
- Horn R. C. Jr. Enterline HT (1958). Rhabdomyosarcoma a clincopathological study and classification Cancer11, 181.
- Masson J. K. and Soule EH (1965). Embryonal rhabdomyosar coma of Head and Neck. American Journal of Surgery 110,585.
- Stout A. D. (1946). Rhabdomyosarcomas of the skeletal muscles. Annals of Surgery 123,447.
- Vieta L. R. Guraieb SR and Obregon MA (1962) Archives of Otolaryngology 75,248.
- Wilis R. A. (1967) Pathology of Tumors 4th edition. Editorial Butterworth, London.
* Rhabdomyosarcoma mostly leads to a conspicuous lumpy appearance on the body of the child.
* In case the tumor is internally situated, then the symptoms arising would be dependent on its site. For instance, tumors that develop in the nasal passage could exert strain on the Eustachian tubes; tumor arising in the orbit of the eyes known as orbital tumor could make the eyes appear protruding whereas a tumor located in the bladder could lead to difficulty in urination.
I felt pity when I read that this kind of condition has a prognosis of 10% only.
Management include surgery, chemotherapy, and radiation therapy..at an early age this kind of management may be a great interference for the growth of the child. And the prognosis is just only 10 %...!! Prevention and early detection of this condition can a great help to the child or to the patient.
My best friends 8 year old daughter very sadly passed away last May of nasophatyngeal rhabdomyosarcoma. She was misdiagnosed with various problems relating to her hearing, inability to swallow 5 times, and then her face become swollen on one side and one of her pupils stopped moving. They then detected a lemon sized tumour which was visible from looking up her nose.
She began an immediate course of radio and chemo therapies, however tests showed that due to how late the cancer was detected, it had spread to her chest, spine and lungs. She fought very very hard and remained strong until given the all clear, however, she was still suffering from immense back pain. Her doctor took her off of the pain meds implying that the pain was pyscho symatic and after some convincing, they performed a lumber punch which identified cancer in her bone marrow, and she was given days. She passed 2 weeks prior to her 9th birthday (also her mothers birthday) in her mummy's arms. She is very sadly missed. We were each told of the mortality rate and the chances however, the treatment in itself was very badly arranged and the doctor in charge at the local hospital, unprofessional. The doctor who misdiagnosed her has now issued a formal apology but I believe that more research and awareness should be made about Rhabdomyosarcomas as it is barely heard of.
Ironically, another young girl has been recently diagnosed and treated in Cambridge for the exact type of cancer. I just hope the poor little one has better administered treatment than my friends poor little one.